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Table 2 COVID-19- and SARS-related hospital mortality in patients with different rare diseases

From: Hospital mortality in patients with rare diseases during pandemics: lessons learnt from the COVID-19 and SARS pandemics

 

Admitted with COVID-19 infection

Admitted with SARS infection

 

Number of admission (%)

Number of people (%)

Number of episode deaths (%)

Mortality rate

Number of admission (%)

Number of people (%)

Number of episode deaths (%)

Mortality rate

Rare abdominal surgical disease

0 (0.0)

0 (0.0)

0 (0.0)

0.0

0 (0.0)

0 (0.0)

0 (0.0)

0.0

Rare bone disease

1 (1.1)

1 (1.3)

0 (0.0)

0.0

0 (0.0)

0 (0.0)

0 (0.0)

0.0

Rare cardiac disease

2 (2.1)

2 (2.6)

0 (0.0)

0.0

3 (3.6)

3 (5.5)

2 (28.6)

66.7

Rare circulatory system disease

0 (0.0)

0 (0.0)

0 (0.0)

0.0

0 (0.0)

0 (0.0)

0 (0.0)

0.0

Rare developmental defect during embryogenesis disease

23 (24.2)

19 (24.7)

0 (0.0)

0.0

4 (4.8)

3 (5.5)

0 (0.0)

0.0

Rare endocrine disease

10 (10.5)

9 (11.7)

0 (0.0)

0.0

3 (3.6)

3 (5.5)

0 (0.0)

0.0

Rare eye disease

2 (2.1)

2 (2.6)

0 (0.0)

0.0

0 (0.0)

0 (0.0)

0 (0.0)

0.0

Rare gastroenterologic disease

0 (0.0)

0 (0.0)

0 (0.0)

0.0

2 (2.4)

2 (3.6)

0 (0.0)

0.0

Rare gynaecologic or obstetric disease

0 (0.0)

0 (0.0)

0 (0.0)

0.0

0 (0.0)

0 (0.0)

0 (0.0)

0.0

Rare haematology disease

19 (20.0)

15 (19.5)

0 (0.0)

0.0

34 (41.0)

24 (43.6)

2 (28.6)

8.3

Rare hepatic disease

1 (1.1)

1 (1.3)

1 (20.0)

100.0

0 (0.0)

0 (0.0)

0 (0.0)

0.0

Rare inborn errors of metabolism

3 (3.2)

3 (3.9)

2 (40.0)

66.7

3 (3.6)

2 (3.6)

0 (0.0)

0.0

Rare immune disease

0 (0.0)

0 (0.0)

0 (0.0)

0.0

0 (0.0)

0 (0.0)

0 (0.0)

0.0

Rare neoplastic disease

7 (7.4)

5 (6.5)

1 (20.0)

20.0

6 (7.2)

5 (9.1)

2 (28.6)

40.0

Rare neurologic disease

22 (23.2)

16 (20.8)

1 (20.0)

6.3

21 (25.3)

9 (16.4)

1 (14.3)

11.1

Rare odontologic disease

0 (0.0)

0 (0.0)

0 (0.0)

0.0

0 (0.0)

0 (0.0)

0 (0.0)

0.0

Rare otorhinolaryngologic disease

9 (9.5)

7 (9.1)

0 (0.0)

0.0

3 (3.6)

2 (3.6)

0 (0.0)

0.0

Rare renal disease

1 (1.1)

1 (1.3)

0 (0.0)

0.0

0 (0.0)

0 (0.0)

0 (0.0)

0.0

Rare respiratory disease

3 (3.2)

3 (3.9)

0 (0.0)

0.0

0 (0.0)

0 (0.0)

0 (0.0)

0.0

Rare skin disease

2 (2.1)

2 (2.6)

0 (0.0)

0.0

0 (0.0)

0 (0.0)

0 (0.0)

0.0

Rare systemic or rheumatologic disease

2 (2.1)

2 (2.6)

0 (0.0)

0.0

4 (4.8)

2 (3.6)

0 (0.0)

0.0

Rare urogenital disease

0 (0.0)

0 (0.0)

0 (0.0)

0.0

0 (0.0)

0 (0.0)

0 (0.0)

0.0

Unique total

95

77a

5

6.5

77

50a

6a

12.0

  1. aSome patients had rare disease diagnosis from two or more rare disease categories