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Table 3 Characteristics of the sample and results of the 7 cases: 1* Type of MPS: I—Hurley Syndrome, II—Hunter Syndrome, III—Sanfilippo Syndrome, IV—Mórquio Syndrome, V—Scheie Syndrome, VI—Maroteaux-Lamy Syndrome; 2* age in years at surgery; 3* Complementary Exams performed before the surgery. EMG = electromyography. US = Ultrasound; 4* AFL = Assessment of the Functional Level: 5* Negative = 0, Positive = 1. Assessment after 12 month of surgery (mean)

From: Functional results after carpal tunnel release in mucopolysaccharidosis

Patient

MPS type (1)

Age at surgery (2)

Exams (3)

AFL Preop (4)

Preop wrinkle test (5)

Follow-up (6)

AFL Postop (4)

Postop wrinkle test (5)

1

I

4.58

EMG/US

II

0

13

IV

1

2

II

12.8

EMG/US

III

1

13

IV

1

3

IV

11.4

EMG/US

II

0

12

IV

1

4

II

8.17

US

III

0

11

III

0

5

II

9.75

US

III

0

10

IV

1

6

II

5.92

III

0

13

IV

1

7

II

12

IV

1

12

V

1