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Table 3 Characteristics of the sample and results of the 7 cases: 1* Type of MPS: I—Hurley Syndrome, II—Hunter Syndrome, III—Sanfilippo Syndrome, IV—Mórquio Syndrome, V—Scheie Syndrome, VI—Maroteaux-Lamy Syndrome; 2* age in years at surgery; 3* Complementary Exams performed before the surgery. EMG = electromyography. US = Ultrasound; 4* AFL = Assessment of the Functional Level: 5* Negative = 0, Positive = 1. Assessment after 12 month of surgery (mean)

From: Functional results after carpal tunnel release in mucopolysaccharidosis

Patient MPS type (1) Age at surgery (2) Exams (3) AFL Preop (4) Preop wrinkle test (5) Follow-up (6) AFL Postop (4) Postop wrinkle test (5)
1 I 4.58 EMG/US II 0 13 IV 1
2 II 12.8 EMG/US III 1 13 IV 1
3 IV 11.4 EMG/US II 0 12 IV 1
4 II 8.17 US III 0 11 III 0
5 II 9.75 US III 0 10 IV 1
6 II 5.92 III 0 13 IV 1
7 II 12 IV 1 12 V 1