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Table 1 Classification of the mucopolysaccharidoses

From: Functional results after carpal tunnel release in mucopolysaccharidosis

Name of the syndrome GAG substrates
MPS I Dermatan sulphate
Hurley, Hurley-Scheie and Scheie syndromes Heparan sulphate
MPS II Dermatan sulphate
Hunter syndrome Heparan sulphate
MPS III Heparan sulphate
Sanfilippo syndrome  
MPS IV Keratan sulphate
Morquio syndrome  
MPS VI Dermatan sulphate
Marateaux-Lamy syndrome  
MPS VII Dermatan sulphate
Sly syndrome Heparan sulphate
MPS IX Hyaluronan
Natowicz disease