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Table 1 Classification of the mucopolysaccharidoses

From: Functional results after carpal tunnel release in mucopolysaccharidosis

Name of the syndrome

GAG substrates

MPS I

Dermatan sulphate

Hurley, Hurley-Scheie and Scheie syndromes

Heparan sulphate

MPS II

Dermatan sulphate

Hunter syndrome

Heparan sulphate

MPS III

Heparan sulphate

Sanfilippo syndrome

 

MPS IV

Keratan sulphate

Morquio syndrome

 

MPS VI

Dermatan sulphate

Marateaux-Lamy syndrome

 

MPS VII

Dermatan sulphate

Sly syndrome

Heparan sulphate

MPS IX

Hyaluronan

Natowicz disease