Table 1 The prevalence of APS1 (n = 13) related components
Components | Prevalence (%) |
|---|---|
Classic triad | |
Hypoparathyroidism | 12 (92.3) |
Chronic mucocutaneous candidiasis | 9 (69.2) |
Addison’s disease | 9 (69.2) |
Any of two | 5 (38.5) |
All three | 6 (46.2) |
Other endocrinopathies | |
Subclinical hypothyroidism | 6 (46.1) |
Primary amenorrhea | 2 (15.4) |
Ectodermal dysplasia | |
Enamel dysplasia and nail dystrophy | 6 (46.1) |
Hair loss | 8 (61.5) |
Ocular manifestations | |
Keratitis | 1 (7.7) |
Retinitis pigmentation | 2 (15.4) |
Hematological diseases | |
Myeloproliferative disease | 1 (7.7) |
Pure red cell aplasia | 1 (7.7) |
Other less common complications | |
Intestinal malabsorption | 3 (23.1) |
Renal tubular acidosis | 1 (7.7) |
Asplenia | 1 (7.7) |
Autoimmune hepatitis | 1 (7.7) |
Ankylosing spondylitis | 1 (7.7) |