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Table 5 Pulmonary function parameters in patients with BHDS ( VC, vital capacity; FEV1,-force

From: Novel folliculin gene mutations in Polish patients with Birt–Hogg–Dubé syndrome

Family Patient VC% pred VC (L) FEV1 (%pred) FEV1 (L) TLC (%pred) TLC (L) RV (%pred)) RV(L) Tl,co Tl,co (%pred) TVPG (mmHg)
1 1.1 85 3.83 87 3.1 86 5.62 86 1.79 7.77 81 21
2 2.1 120 3.5 110 2.5 No No No No No No No
  2.2 121 3.6 103 2.5 No No No No No No No
  2.3 110 4.1 100 3.6 No No No No No No No
3 3.1 80 1.94 68 1.3 96 4.06 133 2.43 3.75 60 28
4 4.1 90 3.0 91 2.4 104 5.22 121 2.22 5.65 81 21
5 5.1 91 3.0 86 2.4 103 5.57 129 2.42 8.08 93 No
  5.2 86 3.15 102 2.58 102 5.55 86 1.53 9.25 102 No
6 6.1 102 3.65 95 2.35 116 5.65 132 2.55 5.97 80 26
7 7.1          No No No
8 8.1 116 3.37 116 2.7 123 6.2 127 2.3 5.88 73 21
  8.2 120 4.99 120 4.19 129 6.88 130 1.89 6.99 72 No
9 9.1 102 3.63 99 2.83 112 5.84 120 2.21 6.78 81 22
10 10.1 96 3.65 86 2.69 113 5.79 133 2.3 7.49 85 21
  10.2            
Mean (SD)   102.0 ± 15.1 3.45 ± 0.69 96.9 ± 14.6 2.68 ± 0.66 108.4 ± 12.8 5.64 ± 0.7 119.7 ± 18.33 2.16 ± 0.32 6.76 ± 1.53 80.8 ± 11.48 22.86 ± 2.9