|
Age (years)
|
56.0 (13.2)
|
55.5 (7.8)
|
|
< 65
|
10 (76.9%)
|
9 (81.8%)
|
|
≥ 65
|
3 (23.1%)
|
2 (18.2%)
|
|
Female sex
|
6 (46.2%)
|
6 (54.5%)
|
|
Height (m)
|
1.642 (0.085)
|
1.643 (0.099)
|
|
Weight (kg)
|
54.97 (9.16)
|
59.15 (14.67)
|
|
Body mass index (kg/m2)
|
20.38 (2.85)
|
21.67 (3.89)
|
|
Blood pressure (mm Hg)
|
128.7 (8.5)/84.7 (13.6)
|
118.2 (15.6) / 72.9 (10.0)
|
|
Heart rate (beats/min)
|
75.0 (9.3)
|
75.6 (8.0)
|
|
Abnormal ECG
|
4 (30.8%)
|
5 (45.5%)
|
|
Other neurological abnormal findings
|
0 (0%)
|
0 (0%)
|
|
Muscle CT findings consistent with the target disease
|
13 (100%)
|
11 (100%)
|
|
Previous diseases
|
0
|
0
|
|
Concurrent diseases
|
12 (92.3%)
|
9 (81.8%)
|
|
Number of targeted neuromuscular diseases
| | |
|
Spinal muscular atrophy
|
3
|
2
|
|
Spinal bulbar muscular atrophy
|
2
|
0
|
|
Amyotrophic lateral sclerosis
|
1
|
0
|
|
Charcot Marie Tooth disease
|
1
|
2
|
|
Myotonic dystrophy
|
0
|
2
|
|
Distal myopathy with RV
|
0
|
1
|
|
Distal myopathy, Myoshi
|
2
|
2
|
|
FSH-type muscular dystrophy
|
2
|
1
|
|
Other limb girdle-type muscular dystrophy
|
1
|
1
|
|
Sporadic inclusion body myositis
|
1
|
0
|
|
Concomitant treatment, medication
|
13 (100%)
|
11 (100%)
|
|
Other rehabilitation programs
|
9 (69.2%)
|
8 (72.7%)
|
|
Outpatient during treatment periods
|
8 (61.5%)
|
2 (18.2%)
|
|
2MWT (metres)
|
63.258 (30.457)
|
67.257 (25.508)
|
|
Barthel index (total score: 0–100)
|
75.4 (21.0)
|
84.5 (11.9)
|
|
Total Manual Muscle Test (MMT) scores (0–60)
|
31.12 (5.57)
|
30.59 (3.64)
|
