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Table 2 Demographic characteristics among different causes of DCLD

From: The etiology of diffuse cystic lung diseases: an analysis of 1010 consecutive cases in a LAM clinic

  Numbers Age (years) Female (%) Smoking history Family history
LAM 711 38.2 ± 10.8 711(100.0%) 1.1% 1.1%
BHD 46 47.3 ± 10.4 42 (91.3%) 6.5% 80.4%
SS 38 49.7 ± 10.4 38 (100.0%) 2.6% 5.3%
PLCH 14 32.8 ± 12.4 6 (42.9%) 92.9% 0
Tumor 3 41–50 3 (100.0%) 0 0
CD 2 34–46 1 (50%) 50% 0
AVA 2 37–51 2 (100%) 0 0
SLE 1 45 1 (100%) 0 0
MFS 1 57 0 0 100.0%
AMY 1 32 1 (100.0%) 0 0
CCAM 1 28 1 (100.0%) 0 0
PPFE 1 37 1 (100.0%) 0 0
  1. AMY amyloidosis, AVA antineutrophil cytoplasmic antibody-associated vasculitis, BHD Birt–Hogg–Dubé syndrome, CCAM congenital cystic adenomatoid malformation of the lung, CD Castleman disease, DCLD diffuse cystic lung disease, LAM lymphangioleiomyomatosis, MFS Marfan syndrome, PPFE pleuroparenchymal fibroelastosis, PLCH pulmonary Langerhans cell histiocytosis, SS Sjogren's syndrome