Skip to main content
Fig. 2 | Orphanet Journal of Rare Diseases

Fig. 2

From: The etiology of diffuse cystic lung diseases: an analysis of 1010 consecutive cases in a LAM clinic

Fig. 2

Typical images of DCLD on CT scans are suggestive of a diagnosis. A A typical lymphangioleiomyomatosis (LAM) image in a 38-year-old woman shows a evenly distributed diffuse thin-walled cysts crossover all lung fields. Pneumothorax and chylothorax are frequently seen (not shown) in patients with LAM. (2) A typical Birt–Hogg–Dubé syndrome image in a 63-year-old woman shows large and irregular cysts frequently distributed in the lower lung fields and subpleural or paramediastinal regions. (3) A typical pulmonary Langerhans cell histiocytosis (PLCH) image in a 32-year-old woman with a history of cigarette smoking shows upper and middle lung field dominant distribution with irregular cysts and multiple nodules. Costophrenic regions are likely less involved (not shown). (4) A 66-year-old women with a history of Sjogren syndrome was found diffuse cystic changes in the lung. Images on CT show randomly distributed cysts that are larger than cysts usually presented in LAM as well as patchy infiltrates and nodules. Light chain deposition disease was diagnosed after thoracoscopic lung biopsy

Back to article page