Fig. 2

Age at LOA or mortality: a mean/median age at LOA; b LOA over time, c mean/median age at mortality; and d Mortality over time. LOA = loss of ambulation; CS = corticosteroid; LT = long-term; NR = not reported; ST = short term; yrs = years DFZ = deflazacort; NR = not reported; Pred = prednisone; yrs = years; CINRG-DNHS = The Cooperative International Neuromuscular Research Group Duchene Natural History Study; MD STARnet = Muscular Dystrophy Surveillance, Tracking, and Research Network; CM = cardiomyopathy; CPT = cardiopulmonary therapies; Died RF = died from respiratory failure; Died CF = died cardiac failure; Died Oth = died from other causes; IV = invasive ventilation; LVD = left ventricular dysfunction; NIV = non-invasive ventilation; CV = cardiovascular. Notes **Middle value in range of medians. Long follow up = 10–20 years; median follow up = 5.4–7.1 years; short follow up = 1.9–2 years; unknown = not reported