Skip to main content

Table 4 Diagnostic criteria of relapsing polychondritis used in present study

From: Clinical patterns and the evolution of relapsing polychondritis based on organ involvement: a Chinese retrospective cohort study

Criteria

Items of criteria

Requirement

McAdam’s criteria [14]

Bilateral auricular chondritis

Nasal chondritis

Respiratory tract chondritis

Non-erosive seronegative polyarthritis

Ocular inflammation

Cochlear and/or vestibular dysfunction

3 out of 6 criteria

Damiani’s criteria [15]

3 of 6 McAdam et al. criteria

1 of 6 McAdam et al. criteria + histologic confirmation

2of 6 McAdam et al. criteria + Response to corticosteroids or dapsone

Any of these

Michet’s criteria [16]

Major criteria:

 Auricular cartilage inflammation

 Nasal cartilage inflammation

 Laryngotracheal cartilage inflammation

Minor criteria:

 Ocular inflammation

 Hearing loss

 Vestibulary dysfunction

 Seronegative arthritis

2 major criteria

or

1 major criteria + 2 minor criteria

Criteria of Partial RPC [11]

A. Recurrent chondritis with deformity

B. Vestibular dysfunction

C. Ocular inflammation

D. Inflammatory arthritis

A + any of B to D

Criteria of Limited RPC [6, 8, 13, 17,18,19,20,21,22,23,24]

A. Recurrent inflammatory episodes at isolated cartilaginous sites

B. Exclusion of other possible causes

C. Responsive to glucocorticoids

A + B + C