Table 2 Classification based on organ involvement pattern
Organ involvement | At disease onset | During follow-up | ||||
|---|---|---|---|---|---|---|
Ear | Airway | Limited | Systemic | Limited | Systemic | |
Subgroup A | + | − | 35 (27.8) | 29 (23.0) | 25 (19.8) | 37 (29.4) |
Subgroup B | − | + | 31 (24.6) | 18 (14.3) | 26 (20.6) | 22 (17.5) |
Subgroup C | + | + | 0 (0) | 6 (4.8) | 0 (0) | 13 (10.3) |
Subgroup D | − | − | 0 (0) | 7 (5.6) | 0 (0) | 3 (2.4) |