Table 1 Summary of disease stages
Disease stage | CLN2 clinical rating scale score (motor score + language score) | Additional characteristics |
|---|---|---|
6 | 6 (3 + 3) | None |
5 | 5 (2 + 3) | None |
4 | 4 (2 + 2) | None |
3 | 3 (1 + 2) | None |
2 | 2 (1 + 1) | None |
1 | 1 (1 + 0) | None |
0 | 0 | None |
0 + VL | 0 | With vision loss |
0 + VL + PC | 0 | With vision loss and requiring palliative care |