Table 1 Classification of disease type families and affected children
Type of MLD | |||||
|---|---|---|---|---|---|
Late-infantile (< 2½ years at onset) | Juvenile (2½ to 16 years at onset) | Adult (> 16 years at onset) | PCH2 | Total | |
Families (n) | 8 | 18 | 1 | 16 | 43 |
Mothers (n) | 8 | 16 | 1 | 16 | 41 |
single mothers (n) | 1 | 3 | 0 | 1 | 5 |
Fathers (n) | 7 | 14 | 1 | 13 | 35 |
Children (n) | 8 | 21 | 1 | 19 | 49 (25♀/24♂) |
age in yrs. at time of surveya | 5.8 (3.1–8.4) | 19.1 (3.2–41.4) | 31.1 (31.1–31.1) | 9.9 (0.8–20.0) | 11.6 (0.8–41.4) |