Table 10 Nutritional Care Interventions in CLN2, statements and consensus data

Any patients affected by CLN2 should be fed according to his/her CNS grade of integrity, or there is no evidence to support feeding CLN2 patients different to any other patient affected by a neurodegenerative disease

38

D

86

For CLN2 patients over age 16 years with significant dysphagia, enteral tube feeding should be considered according to current NICE guidance: https://www.nice.org.uk/guidance/cg32/chapter/1-Guidance#enteral-tube-feeding-in-hospital-and-the-community

35

NA

83

Tube feeding should be considered if one of the following is present: Increased risk of choking, Inability to meet nutritional requirements, Confirmed silent aspiration on video fluoroscopy, Repeated episodes of aspiration pneumonia confirmed by imaging

40

NA

94