Parameter | HeFH (n = 10) | HoFH (n = 4) | ||||
---|---|---|---|---|---|---|
Lipids, mmol/l | Before LA | After LA | Decrease, n (%) patients | Before LA | After LA | Decrease, n (%) patients |
TC | 5.69 (1.16) | 1.93 (0.59)*** | 10 (100) | 7.09 (2.15) | 1.95 (0.66)*** | 4 (100) |
LDLC | 3.57 (1.19) | 0.75 (0.54)*** | 10 (100) | 5.13 (1.87) | 0.85 (0.94)*** | 4 (100) |
HDLC | 1.34 (0.65) | 0.91 (0.33)*** | 10 (100) | 1.51 (0.72) | 1.15 (0.39)*** | 4 (100) |
ApoB | 1.11 (0.28) | 0.28 (0.22)*** | 10 (100) | 1.22 (0.50) | 0.18 (0.17)*** | 4 (100) |
Endoglin, ng/mL | 6.45 (1.85) | 5.56 (1.75)*** | 8 (80) | 6.22 (1.73) | 4.85 (1.80)*** | 3 (75) |
CD40L, pg/mL | 5323 (2059) | 5367 (3093) | 4 (40) | 5177 (1585) | 4239 (1892) | 2 (50) |
hsCRP, mg/L | 2.84 (1.51) | 2.39 (1.38) | 6 (60) | 2.21 (1.36) | 1.82 (1.27) | 3 (75) |
MCP-1, pg/mL | 321.8 (99.2) | 274.5 (86.1) | 6 (60) | 265.6 (71.0) | 221.4 (68.2) | 3 (75) |
sP-selectin, ng/mL | 148.1 (50.7) | 131.7 (53.8)* | 7 (70) | 145.6 (70.6) | 154.3 (212.2) | 3 (75) |