Table 4 Ranking of 5 most important domains in the web survey
From: Validation of the 5-domain Niemann-Pick type C Clinical Severity Scale
# Times ranked n (% of row total) | # Times in Top 5 n (% of total participants [n = 49]) | |||||
|---|---|---|---|---|---|---|
First | Second | Third | Fourth | Fifth | ||
Ambulation | 10 (24.4) | 12 (29.3) | 9 (22.0) | 4 (9.8) | 6 (14.6) | 41 (83.7) |
Swallow | 8 (22.9) | 6 (17.1) | 8 (22.9) | 8 (22.9) | 5 (14.3) | 35 (71.4) |
Speech | 1 (3.1) | 4 (12.5) | 9 (28.1) | 8 (25.0) | 10 (31.3) | 32 (65.3) |
Memory | 3 (10.7) | 4 (14.3) | 5 (17.9) | 9 (32.1) | 7 (25.0) | 28 (57.1) |
Cognition | 8 (34.8) | 4 (17.4) | 4 (17.4) | 4 (17.4) | 3 (13.0) | 23 (46.3) |
Fine motor skills | 2 (9.1) | 8 (36.4) | 2 (9.1) | 5 (22.7) | 5 (22.7) | 22 (44.9) |
Eye movement | 2 (10.5) | 3 (15.8) | 5 (26.3) | 2 (10.5) | 7 (36.8) | 19 (38.8) |
Seizures | 8 (57.1) | 1 (7.1) | 0 | 3 (21.4) | 2 (14.3) | 14 (28.6) |
Hearing | 2 (18.2) | 3 (27.3) | 3 (27.3) | 1 (9.1) | 2 (18.2) | 11 (22.4) |