Parameter | Value |
---|---|
Country, n (%) | |
France | 58 (24.0) |
United Kingdom | 57 (23.6) |
Spain | 39 (16.1) |
Canada | 32 (13.2) |
Australia | 28 (11.6) |
Switzerland | 8 (3.3) |
Germany | 7 (2.9) |
Austria | 13 (5.4) |
Age, years | |
Mean (SD) | 43.8 (14.7) |
Range | 18–92 |
Sex, n (%) | |
Female | 163 (67.4) |
Male | 78 (32.2) |
Not indicated | 1 (0.4) |
HAE type, n (%) | |
Type 1 | 198 (81.8) |
Type 2 | 44 (18.2) |
Mean (SD) age at onset of first HAE symptoms, years | 11.5 (8.9) |
Mean (SD) age at HAE diagnosis, years | 20.8 (13.2) |
Mean (SD) delay in diagnosis,a years | 9.3 (11.0) |
Family history of HAE, n (%) | |
Yes | 192 (79.3) |
No | 45 (18.6) |
Not sure | 5 (2.1) |
Comorbidities,b n (%) | |
Anxiety | 63 (26.0) |
Gastrointestinal disorder | 43 (17.8) |
Depression | 41 (16.9) |
High cholesterol | 33 (13.6) |
Hypertension | 31 (12.8) |