From: Pancreatic involvement in patients with inborn errors of metabolism
Underlying disease | MMA (Case 1) | MMA (Case 2) | PPA (Case 3) | PPA (Case 4) | FAOD (Case 5) | Hyperornithinemia (Case 6) |
---|---|---|---|---|---|---|
Pancreatitis | ||||||
Pancreatitis |  +  |  +  |  −  |  +  |  +  |  −  |
Amylase during metabolic crisis (IU/L) |  > 4000 | 176–215 | 81–90 | 317–558 | 122–808 |  −  |
Lipase (range) |  > 4000 | 100 |  −  | 347–1585 | 493–13,978 |  −  |
Onset of AP | 15 y | 19 y |  −  | 4 y | 10 y |  −  |
No. of episodes | 7 | 1 | 1 | 5 | 1 | None |
Diabetes mellitus (DM) | ||||||
DM |  +  |  −  |  +  |  +  |  −  |  +  |
DM_onset | 20 y |  −  | 14 y | 8 y |  −  | 7 y |
DM_management | Insulin |  −  | Insulin | Insulin |  −  | Insulin |