Table 1 Characteristics of the clinical and pulmonary findings in 71 NF1 patients
Characteristics | All NF1 patients n = 71 |
|---|---|
Female gender | 40 (56) |
Age (years ± SD) | 33 ± 14 |
Current smokers | 17 (24) |
MPNST | 30 (42) |
Reticulations | 18 (25) |
GGO | 7 (10) |
Consolidation | 6 (8) |
Emphysema | 22 (31) |
 Centrilobular | 5 (7) |
 Paraseptal | 21 (30) |
 Panlobular | 0 (0) |
Honey combing | 0 (0) |
Tree-in-bud sign | 0 (0) |
Nodules | 23 (32) |
≤ 10 | 18 (25) |
> 10 | 5 (7) |
Max. diameter (mm ± SD) | 5 ± 2 |
Cysts | 25 (35) |
≤ 10 | 18 (25) |
> 10 | 7 (10) |
Max. diameter (mm ± SD) | 8 ± 3 |
UL | 14 (20) |
ML | 2 (3) |
LL | 9 (13) |
Left | 11 (15) |
Right | 14 (20) |
Thickened interlobular septa | 10 (14) |
Pleural effusion | 3 (4) |
Pericardial effusion | 0 (0) |
Pulmonary metastasis | 6 (8) |