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Table 3 Construct validity

From: Fatigability in spinal muscular atrophy: validity and reliability of endurance shuttle tests

 

ESNHPT

ESBBT

ESWT

Discriminative validity

SMA – HC - DC

SMA - HC

SMA - HC

Time to limitation

(Mdn (s))

SMA (N = 55): 937 (48–1200)

HC P1 (N = 15): 600

HC P2 (N = 9): 1200

DC (N = 15): 1200 (967–1200)

SMA (N = 37): 245 (50–1200)

HC P1 (N = 15): 600

HC P2 (N = 5): 1200

SMA (N = 15): 861 (218–1200)

HC P1 (N = 12): 600

HC P2 (N = 8): 1200

Drop-out (%)

SMA: 54.5%

HC: 0%

DC: 6.7%

SMA type 2: 73.3%

SMA type 3a: 63.6%

SMA type 3b: 7.1%

SMA: 70.3%

HC: 5%

SMA type 2: 100%

SMA type 3a: 80%

SMA type 3b-4: 44%

SMA: 73.3%

HC: 0%

Convergent validity

SMA

SMA

SMA

Muscle strength (N)

No decrease

SA: −5.5 (2.1), p = .013

KF: - 8.9, p = .011

Perceived fatigue (0–10)

G: + 1.1 (0.2), p = .000

UA: + 2.6 (0.3), p = .000

LA: + 2.8 (0.4), p = .000

H: + 2.4 (0.4), p = .000

UA: + 2.6 (0.4), p = .000)

LA: + 2.1 (0.4), p = .000

H: + 1.0 (0.3), p = .000

G: +  3.7 (0.77), p = .000

UL: +  4.0 (.92), p = .001

Motor adaptation (Yes)

No drop-out: 26%

Drop-out: 96%

No drop-out: 33%

Drop-out: 96%

No drop-out: 75%

Drop-out: 100%

  1. ESWT Endurance Shuttle Walk Test, ESBBT Endurance Shuttle Box and Block Test, ESNHPT Endurance Shuttle Nine Hole Peg Test, HC Healthy Controls, DC Disease Controls, P1 protocol 600 s, P2 protocol 1200 s, KF Knee Flexion, SA Shoulder Abduction, G General, UL Upper Limb, UA Upper Arm, LA Lower Arm, H Hand