From: Fatigability in spinal muscular atrophy: validity and reliability of endurance shuttle tests
SMA (N = 61) | HC (N = 25) | PC (N = 15) | ||||||
---|---|---|---|---|---|---|---|---|
ESWT (N = 15) | ESBBT (N = 37) | ESNHPT (N = 55) | ESTCS (N = 61) | ESWT (N = 20) | ESBBT (N = 20) | ESNHPT (N = 24) | ESNHPT (N = 15) | |
Subtype/ Diagnosis | 3a: N = 3 3b: N = 11 4: N = 1 | 2: N = 11 3a: N = 10 3b: N = 15 4: N = 1 | 2: N = 30 3a: N = 11 3b: N = 14 | 2: N = 31 3a: N = 14 3b: N = 15 4: N = 1 | NA | NA | NA | LGMD:N = 7 BMD:N = 1 DMD:N = 7 |
Gender (F:M) | 4:11 | 17:20 | 34:21 | 34:27 | 12:8 | 14:6 | 15:9 | 3:12 |
Age (years) | 28.4 (12.4) | 28.4 (14) | 28 (14.4) | 28.7 (14.3) | 21.8 (9.6) | 21.6 (7.9) | 21.1 (9.6) | 14.0 (3.6) |
MRC-scale (44–220) | 191 (15) | 161 (32) | 134 (39) | 138 (39) | 220 (1) | 220 (1) | 220 (1) | 144 (44) |
MRC-scale upper limb (22–110) | 98 (8) | 86 (14) | 75 (18) | 76 (17) | 110 | 110 | 110 | 79 (21) |
Level of ambulation | NA: N = 12 CA: N = 2 HA: N = 1 | NA: N = 12 CA: N = 2 HA: N = 3 NFA: 1 NOA: N = 19 | NA: N = 9 CA: N = 1 HA: N = 2 NFA: 1 NA: N = 42 | NA: N = 12 CA: N = 2 HA: N = 3 NFA: N = 1 NOA: N = 43 | NA: N = 20 | NA: N = 20 | NA: N = 24 | NA: N = 4 CA: N = 3 NOA: N = 8 |