Table 3 Frequencies of late complications in adult Korean patients with GSD Ia
Total patients (n = 26)a | n (%) |
|---|---|
Hepatomegaly | 26 (100%) |
Dyslipidemia | 26 (100%) |
Hepatic adenoma | 14 (54%) |
Renal complication | 13 (50%) |
Osteopenia or fracture | 12 (46%) |
Short stature (SDS: < −2.0) | 12 (46%) |
Anemia | 12 (46%) |
Delayed puberty | 11 (42%) |
Gout | 7 (27%) |
Pulmonary hypertension | 2 (8%) |
Hepatocellular carcinoma | 2 (8%) |