Cardiac characteristics | Glu54Gln ATTR (7 patients) |
---|---|
Age, years | 45.9 |
Sex, % male | 28.5% |
NT-proBNP (pg/ml), mean [range] | 2815.6 [34.5–7140] |
IVS thickness, mm, mean [range] | 16 [13–21] |
PW thickness, mm, mean [range] | 15 [12–17] |
RV free wall thickness, mm, mean [range] | 7 [5–8] |
S′, cm/s, mean [range] | 5.4 [4–7] |
E/A, mean [range] | 2.3 [0.9–4.2] |
E/E’, mean [range] | 19 [10–26] |
TAPSE, mean [range] | 19 [13–26] |
GLS, %, mean [range] | −13 [−7.7, −18.5] |
Atrial fibrillation, n, % | 2 (15%) |
AV block, n, % | 5 (38%) |
RBBB, n, % | 4 (31%) |
LBBB, n, % | 1 (8%) |
LVEF %, mean [range] | 49 [30–60] |
Pericardial effusion, n, % | 2 (15%) |