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Table 1 Patient profiles during hypoglycemia

From: Neonatal hyperinsulinism in transient and classical forms of tyrosinemia

  Patient 1 Patient 2
Laboratory samples (values consistent with hyperinsulinemic hypoglycemia) [7, 13] Transient tyrosinemia of infancy Hereditary tyrosinemia type I
Preserved plasma glucose < 3.3 mmol/L (< 60 mg/dL) 1.9 (34) 2.2 (39)
Beta-hydroxy butyrate < 1.8 mmol/L  < 0.2  < 0.2
C-peptide > 0.002 nmol/L (> 0.5 ng/dL) 0.004 (1.1) 0.007 (2.1)
Insulin > 13.9 pmol/L (> 2 uU/mL) 30.6 (4.4) 20.8 (3)
Growth hormone > 7.5 ug/L (> 7.5 ng/mL) 17 (17) 7.5 (7.5)
Cortisol 496 nmol/L (> 18 mcg/dL) 551.8 (20) 689.7 (25)