Table 1 Patient profiles during hypoglycemia
From: Neonatal hyperinsulinism in transient and classical forms of tyrosinemia
Patient 1 | Patient 2 | |
|---|---|---|
Laboratory samples (values consistent with hyperinsulinemic hypoglycemia) [7, 13] | Transient tyrosinemia of infancy | Hereditary tyrosinemia type I |
Preserved plasma glucose < 3.3 mmol/L (< 60 mg/dL) | 1.9 (34) | 2.2 (39) |
Beta-hydroxy butyrate < 1.8 mmol/L | < 0.2 | < 0.2 |
C-peptide > 0.002 nmol/L (> 0.5 ng/dL) | 0.004 (1.1) | 0.007 (2.1) |
Insulin > 13.9 pmol/L (> 2 uU/mL) | 30.6 (4.4) | 20.8 (3) |
Growth hormone > 7.5 ug/L (> 7.5 ng/mL) | 17 (17) | 7.5 (7.5) |
Cortisol 496 nmol/L (> 18 mcg/dL) | 551.8 (20) | 689.7 (25) |