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Table 4 Differential diagnoses of Behçet diseases according to organ involvement

From: French recommendations for the management of Behçet’s disease

Type of damage

Differential diagnoses

Mucous ulcerations

Herpes, neutropenia, pemphigus, CIID, drugs, vitamin deficiencies

Bipolar aphthosis

CIID, MAGIC syndrome, deficiency of mevalonate kinase, A20 haplo-insufficiency

Articular damage

Spondyloarthropathies

Gastrointestinal damage

CIID, NSAID toxicity, infectious colitis

Venous thrombosis

Thrombophilia, genetic or acquired

Arterial damage

Septic aneurysms, atrophic polychondritis, Takayasu

Neurological damage

SEP, sarcoidosis, tumoral pathologies, lymphomas or infectious meningo-encephalitis