Skip to main content

Table 5 Cardiac data—before and after treatment

From: High output cardiac failure in 3 patients with hereditary hemorrhagic telangiectasia and hepatic vascular malformations, evaluation of treatment

 

Patient 1

Patient 2

Patient 3

Baseline

After OLT

Baseline

After BVZ

Baseline

After BVZ

ECG

      

 Rhythm

AFLI

AFLI

SR

SR

AFLI

AFLI

 Heart rate (bpm)

77

90

95

83

86

74

Echocardiogram

      

 LV size

Normal

Normal

Normal

Normal

Normal

Normal

 LVEF (%)

60

50

60

60

60

60

 Left heart valve disease

No

No

No

No

No

No

 RV size

Normal

Normal

Slight dilatation

Slight dilatation

Moderate dilatation

Moderate dilatation

 TAPSE (mm)

34

14

31

24

17

20

 TR size

Mild

Mild

Moderate

Moderate

Moderate

Moderate

 TRG (mmHg)

43

30

36

41

65

39

RHC

      

 PCWP (mmHg)

18

NA

18

21

22

14

 PAP, systolic (mmHg)

43

NA

52

60

78

51

 PAP, diastolic (mmHg)

23

NA

21

21

32

22

 PAP, mean (mmHg)

32

NA

38

40

48

32

 RVP, systolic (mmHg)

42

NA

48

60

78

51

 RVP, diastolic (mmHg)

10

NA

11

15

20

9

 RAP (mmHg)

13

NA

12

12

18

9

 Cardiac output (l/min)

10.2

6.5a

8.5

6.2

7.8

6.4

 Cardiac index (l/min/m2)

6.6

4.5a

5.4

4.4

5.3

4.3

 SVO2 (%)

90

NA

86

81

77

85

 PVR (WU)

1.4

NA

2.4

3.1

3.7

2.8

  1. aPerioperative
  2. OLT orthotopic liver transplantation, BVZ bevacizumab, AFLI atrial fibrillation, SR sinus rhythm, bpm beats per minute, LV left ventricular, LVEF left ventricular ejection fraction, RV right ventricular, TAPSE tricuspid annular plane systolic excursion, TR tricuspid valve regurgitation, TRG max tricuspid regurgitation gradient, RHC right heart catheterization, PCWP pulmonary wedge pressure, NA not available, PAP pulmonary arterial pressure, RVP right ventricular pressure, RA right atrium pressure, SVO2 pulmonic arterial oxygen saturation, PVR pulmonary vascular resistance, WU wood units