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Table 1 Clinical, serology and pathology features of 7 RDD mimic IgG4-RD patients

From: Rosai–Dorfman disease mimicking IgG4-related diseases: a single-center experience in China

Sequence number Sex Age Organ involvement/symptom Serology Pathology Treatment Prognosis
IgG1 (mg/L) IgG2 (mg/L) IgG3 (mg/L) IgG4 (mg/L) IgG4 (cells/hpf) IgG4/IgG (%)
1 M 56 Spinal pachymeningitis/numbness, walking unstable 5380 5960 420 4385 > 50 10–30 Glucocorticoids + cyclophosphamide Improved
2 M 63 Liver mass, rash, lacrimal gland swollen 6450 7570 160 6410 10–20 10 Glucocorticoids + cyclophosphamide Improved
3 M 61 Intraspinal mass/skin numbness 5380 5960 420 5800 > 50 40 Glucocorticoids + cyclophosphamide/azathioprine Improved
4 M 50 Pachymeningitis/impaired vision and hearning 8000 2030 110 292 30 20 Glucocorticoids + rituximab (intrathecal injection) Improved
5 M 29 Pachymeningitis (epilepsia)/subcutanous mass 8200 4230 318 1360 > 50 40 Glucocorticoids + cyclophosphamide Improved
6 M 56 Pancreas and duodenum masses/lymph node enlargement 12,600 12,800 763 54,100 > 100 > 40 Glucocorticoids Improved
7 M 37 Sellar region and orbital cavity mass/impaired vision, sinusitis 8310 5880 582 3510 > 100 > 40 None Remain the same
  1. M, male