Male (n = 167) | Female (n = 107) | All (n = 274) | |
---|---|---|---|
No amyloidosis | 80 (48%) | 62 (58%) | 142 (52%) |
TTR mutation | 22 (28%) | 31 (50%) | 53 (37%) |
No TTR mutation | 58 (72%) | 31 (50%) | 89 (63%) |
Amyloidosis | 87 (52%) | 45 (42%) | 132 (48%) |
ATTRv amyloidosis | 82 (94%) | 41 (91%) | 123 (93%) |
Dx before 2006 | 10 (12%) | 9 (22%) | 19 (16%) |
ATTRV30M | 69 (84%) | 31 (76%) | 100 (81%) |
Other mutationa | 3 (4%) | 1 (2%) | 4 (3%) |
ATTRwt amyloidosis | 1 (1%) | 0 (0%) | 1 (1%) |
AL amyloidosis | 4 (5%) | 3 (7%) | 7 (5%) |
Localized | 3 (75%) | 3 (100%) | 6 (86%) |
Systemic | 1 (25%) | 0 (0%) | 1 (14%) |
Gelsolin amyloidosis | 0 (0%) | 1 (2%) | 1 (1%) |