MPS I (n = 8) | MPS II (n = 8) | MPS III (n = 18) | Overall (n = 34) | |||||
---|---|---|---|---|---|---|---|---|
mean n | SD (%) | mean n | SD (%) | mean n | SD (%) | mean n | SD (%) | |
Age | 8.2 | 4.0 | 6.8 | 4.5 | 9.8 | 4.1 | 8.7 | 4.2 |
Gender | ||||||||
f | 6 | (75.0) | 0 | (0.0) | 10 | (55.6) | 16 | (47.1) |
m | 2 | (25.0) | 8 | (100) | 8 | (44.4) | 18 | (52.9) |
Age at first symptoms (yrs) | 0.5 | 0.4 | 0.9 | 0.6 | 2.0 | 2.1 | 1.4 | 1.7 |
Age at diagnosis (yrs) | 1.8 | 2.0 | 2.2 | 0.9 | 4.5 | 2.4 | 3.3 | 2.3 |
Developmental delay | 8 | (100) | 8 | (100) | 18 | (100) | 34 | (100) |
Developmental regression | 4 | (50.0) | 4 | (50.0) | 15 | (83.3) | 23 | (67.7) |
Ability Score | 5.4 | 0.5 | 4.5 | 2.1 | 3.4 | 1.9 | 4.2 | 1.9 |
Mobility | 1.5 | 0.5 | 1.6 | 0.7 | 1.2 | 0.9 | 1.4 | 0.8 |
Speech | 1.9 | 0.4 | 1.3 | 0.9 | 0.7 | 0.8 | 1.1 | 0.9 |
Feeding | 2.0 | 0.0 | 1.6 | 0.7 | 1.6 | 0.6 | 1.7 | 0.6 |