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Table 2 The clinical characteristics of Grisel’s syndrome in patients with Kawasaki disease

From: Grisel’s syndrome in Kawasaki disease

Patient

1

2

3

4

5

6

7

8

9

10

Age(years), Sex

6.6, F

5.7, M

3.7, F

7.2, F

6.3, F

6.2, M

7.3, F

3.5, F

4.5, F

5.2, F

Initial admitted Department

Neurology

Surgeon

Cardiology

Cardiology

Surgeon

Cardiology

Cardiology

Cardiology

Cardiology

Cardiology

Primary diagnosis

Lymphnoditis, Aseptic meningitis

Lymphnoditis

Lymphnoditis

Lymphnoditis

Lymphnoditis, GS

Lymphnoditis, GS

Lymphnoditis

Lymphnoditis

Tonsillitis

Lymphnoditis

Days before the diagnosis of GS

5

5

2

6

4

8

10

4

7

8

Days before the diagnosis of KD

7

8

5

6

5

8

6

6

7

6

Fever days before IVIG treatment

7

9

5

6

6

9

7

6

9

7

Principal clinical features of KD

1, 2, 3, 6

1, 2, 5, 6

1, 3, 5, 6

1,3, 6

2, 3, 6

1,2,3,4, 6

1,2,3,5,6

1,2,3,4,5,6

1, 2, 4, 5, 6

1, 2, 3, 6

Incomplete KD

+

+

+

+

+

+

IVIG resistance

CALs

Clinical features of GS

 Torticollis/Neck pain

+/+

+/+

+/+

+/+

+/+

+/+

+/+

+/+

+/+

+/−

 Lymphadenopathy, size(mm)

Ra, 4.5*5.0

La, 2.5*2.5

L, 3.5*3.0

L, 2.0*2.0

L, 1.5*2.0

L, 1.5*2.5

R, 1.9*3.6

L, 1.8*2.7

R, 2.5*1.6

L, 3.0*4.0

 Fielding classification

Type I

Type III

Type I

Type I

Type III

Type II

Type II

Type I

Type III

Type III

 Rotatory dislocation

Right

Left

Left

Left

Right

Left

Left

Left

Left

Left

 Treatment

Conservative

Conservative

Conservative

Conservative

Conservative

Conservative

Conservative

Conservative

Conservative

Conservative

 Duration treatment

1 month

2 months

14 days

7 days

1.5 months

21 days

21 days

7 days

3 months

2.5 months

  1. Principal clinical features of KD:1. Fever for at least 5 days; 2. Bilateral bulbar conjunctival injection without exudate; 3. Changes in lips and oral cavity;4. Changes in extremities; 5. Polymorphous exanthem; 6. Cervical lymphadenopathy
  2. aR, right side; L, left side