Diagnosis | All (N = 160) | Survival days a | ||||
---|---|---|---|---|---|---|
> 30 days (n = 108) | ≤30 days (n = 46) | ≤7 days (n = 18) | ||||
n(%) | n(%) | n(%) | p value b | n(%) | p value c | |
Underlying/related diseases | ||||||
 Primary HLH | 12 (7.5) | 9 (8.3) | 3 (6.5) | 1 | 3 (16.7) | 0.1375 |
 Autoimmune disorders | 4 (2.5) | 3 (2.8) | 1 (2.2) | 1 | 0 | 1 |
 Malignancy | 8 (5.0) | 6 (5.6) | 2 (4.3) | 1 | 1 (5.6) | 1 |
 EBV infection | 88 (55.0) | 65 (60.2) | 20 (43.5) | 0.0763 | 5 (27.8) | 0.0137 |
 Sepsis | 97 (60.6) | 55 (50.9) | 39 (84.8) | 0.0001 | 17 (94.4) | 0.0018 |
 -Sepsis with confirmed infections | 86 (53.8) | 53 (49.1) | 32 (69.6) | < 0.0001 | 11 (61.1) | < 0.0001 |
 -Sepsis with EBV infection | 48 (30.0) | 31 (28.7) | 16 (34.8) | 0.4520 | 4 (22.2) | 0.4447 |
 Other infections d | 45 (28.1) | 36 (33.3) | 7 (15.2) | 0.0300 | 1 (5.6) | 0.0238 |
Concomitant diagnosis | ||||||
 Myocardial damage | 58 (36.3) | 23 (21.3) | 35 (76.1) | < 0.0001 | 16 (88.9) | < 0.0001 |
 Heart failure | 28 (17.5) | 10 (9.3) | 18 (39.1) | < 0.0001 | 8 (44.4) | 0.0043 |
 Shock | 20 (12.5) | 5 (4.6) | 15 (32.6) | < 0.0001 | 10 (55.6) | < 0.0001 |
 CNS disease | 39 (24.4) | 16 (14.8) | 23 (50.0) | < 0.0001 | 9 (50.0) | 0.016 |
 Hepatic dysfunction | 96 (60.0) | 53 (49.1) | 41 (89.1) | < 0.0001 | 18 (100) | 0.0002 |
 Respiratory failure | 64 (40.0) | 26 (24.1) | 38 (82.6) | < 0.0001 | 16 (88.9) | < 0.0001 |
 ARDS | 13 (8.1) | 3 (2.8) | 10 (21.7) | 0.0003 | 4 (22.2) | 0.0423 |
 Severe pneumonia | 61 (38.1) | 25 (23.1) | 36 (78.3) | < 0.0001 | 13 (72.2) | 0.0016 |
 Coagulopathy | 83 (51.9) | 39 (36.1) | 41 (89.1) | < 0.0001 | 18 (100) | < 0.0001 |
 DIC | 42 (26.3) | 16 (14.8) | 25 (54.3) | < 0.0001 | 12 (66.7) | 0.0002 |
 Acute kidney injury | 17 (10.7) | 5 (4.7) | 12 (26.1) | 0.0003 | 7 (38.9) | 0.0007 |
 Gastrointestinal disorder | 31 (19.4) | 8 (7.4) | 23 (50.0) | < 0.0001 | 8 (44.4) | 0.0089 |
 MODS | 83 (52.2) | 40 (37.4) | 42 (91.3) | < 0.0001 | 18 (100) | < 0.0001 |
 Immunodeficiency | 37 (23.1) | 18 (16.7) | 19 (41.3) | 0.0018 | 6 (33.3) | 0.3714 |