From: Early management of sight threatening retinopathy in incontinentia pigmenti
Included patients | 19 patients (38 eyes) | ||
Age at incontinentia pigmenti diagnosis (days) | Mean 8.9 Median 1 Range [0-44] | ||
Delay between diagnosis and first ophthalmological examination (days) | Mean 5.9 Median 0 Range [0-36] | ||
Age at retinal disease diagnosis (days) | Mean 32.5 Median 19 Range [3-59] | ||
Delay between retinal disease diagnosis and examination under anesthesia (days) | Mean 9 Median 6 Range [3-28] | ||
Retinal manifestations: patients (eyes) | 7 patients (10 eyes) (26.3%) | OD only | 1 patient (1 eye) |
OS only | 3 patients (3 eyes) | ||
OSD | 3 patients (6 eyes) | ||
Duration of follow-up (years) | Mean 6,4 Median 6,0 Range [3-9.8] | ||
Prophylactic ablative therapy | Treated patients | 7 patients (10 eyes) | |
Ablative sessions per eye (mean) | Mean 1.7 Median 2 Range [1-2] | ||
Age at first session (days) | Mean 37 Median 31 Range [22-65] | ||
Delay between 2 sessions (days) | Mean 54.6 Median 61 Range [30-92] | ||
Severe retinal complication (retinal detachement or retinal fold) | 0 |