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Table 1 Clinical findings of patients with incontinentia pigmenti.

From: Early management of sight threatening retinopathy in incontinentia pigmenti

Included patients

19 patients (38 eyes)

Age at incontinentia pigmenti diagnosis (days)

Mean 8.9

Median 1

Range [0-44]

Delay between diagnosis and first ophthalmological examination (days)

Mean 5.9

Median 0

Range [0-36]

Age at retinal disease diagnosis (days)

Mean 32.5

Median 19

Range [3-59]

Delay between retinal disease diagnosis and examination under anesthesia (days)

Mean 9

Median 6

Range [3-28]

Retinal manifestations: patients (eyes)

7 patients (10 eyes)

(26.3%)

OD only

1 patient (1 eye)

OS only

3 patients (3 eyes)

OSD

3 patients (6 eyes)

Duration of follow-up (years)

Mean 6,4

Median 6,0

Range [3-9.8]

  

Prophylactic ablative therapy

Treated patients

7 patients (10 eyes)

 

Ablative sessions

per eye (mean)

Mean 1.7

Median 2

Range [1-2]

 

Age at first session (days)

Mean 37

Median 31

Range [22-65]

 

Delay between 2 sessions (days)

Mean 54.6

Median 61

Range [30-92]

 

Severe retinal complication (retinal detachement or retinal fold)

0