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Table 3 HUI3 Attribute Scores by SMA Type

From: Quality of life data for individuals affected by spinal muscular atrophy: a baseline dataset from the Cure SMA Community Update Survey

Attribute Scores

Type I

Type II

Type III

p value

Vision

 n

29

170

116

0.54

 Mean Score (SD)

0.97 (0.05)

0.97 (0.06)

0.97 (0.03)

 Range

(0.73–1)

(0.59–1)

(0.95–1)

Hearing

 n

30

167

118

0.60

 Mean Score (SD)

0.99 (0.05)

1.0

0.99 (0.05)

 Range

(0.71–1)

(0.48–1)

(0.48–1)

Speech

 n

31

168

118

0.0001*

 Mean Score (SD)

0.51 (0.43)

0.95 (0.11)

0.99 (0.04)

 Range

(0–1)

(0.41–1)

(0.67–1)

Ambulation

 n

31

171

122

0.0001*

 Mean Score (SD)

0.01 (0.06)

0.04 (0.14)

0.32 (0.36)

 Range

(0–0.36)

(0–1)

(0–1)

Dexterity

 n

31

168

120

0.0001*

 Mean Score (SD)

0.13 (0.27)

0.57 (0.35)

0.78 (0.27)

 Range

(0–1)

(0–1)

(0–1)

Emotion

 n

30

166

120

0.10

 Mean Score (SD)

0.94 (0.14)

0.96 (0.08)

0.93 (0.13)

 Range

(0.33–1)

(0.33–1)

(0.33–1)

Cognition

 n

30

167

118

0.001*

 Mean Score (SD)

0.87 (0.25)

0.97 (0.09)

0.96 (0.11)

Range

(0–1)

(0.32–1)

(0.32–1)

Pain

 n

31

169

120

0.09

 Mean Score (SD)

0.90 (0.11)

0.86 (0.16)

0.84 (0.16)

Range

(0.48–1)

(0–1)

(0–1)

  1. *Statistically significant at p < 0.05