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Table 3 HUI3 Attribute Scores by SMA Type

From: Quality of life data for individuals affected by spinal muscular atrophy: a baseline dataset from the Cure SMA Community Update Survey

Attribute Scores Type I Type II Type III p value
Vision
 n 29 170 116 0.54
 Mean Score (SD) 0.97 (0.05) 0.97 (0.06) 0.97 (0.03)
 Range (0.73–1) (0.59–1) (0.95–1)
Hearing
 n 30 167 118 0.60
 Mean Score (SD) 0.99 (0.05) 1.0 0.99 (0.05)
 Range (0.71–1) (0.48–1) (0.48–1)
Speech
 n 31 168 118 0.0001*
 Mean Score (SD) 0.51 (0.43) 0.95 (0.11) 0.99 (0.04)
 Range (0–1) (0.41–1) (0.67–1)
Ambulation
 n 31 171 122 0.0001*
 Mean Score (SD) 0.01 (0.06) 0.04 (0.14) 0.32 (0.36)
 Range (0–0.36) (0–1) (0–1)
Dexterity
 n 31 168 120 0.0001*
 Mean Score (SD) 0.13 (0.27) 0.57 (0.35) 0.78 (0.27)
 Range (0–1) (0–1) (0–1)
Emotion
 n 30 166 120 0.10
 Mean Score (SD) 0.94 (0.14) 0.96 (0.08) 0.93 (0.13)
 Range (0.33–1) (0.33–1) (0.33–1)
Cognition
 n 30 167 118 0.001*
 Mean Score (SD) 0.87 (0.25) 0.97 (0.09) 0.96 (0.11)
Range (0–1) (0.32–1) (0.32–1)
Pain
 n 31 169 120 0.09
 Mean Score (SD) 0.90 (0.11) 0.86 (0.16) 0.84 (0.16)
Range (0.48–1) (0–1) (0–1)
  1. *Statistically significant at p < 0.05