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Table 2 HUI3 Scores by Functional Milestone and SMA Type

From: Quality of life data for individuals affected by spinal muscular atrophy: a baseline dataset from the Cure SMA Community Update Survey

Functional Status Type I Type II Type III
Permanent Ventilation
 n 18 9 0
 Mean Score (SD) − 0.05 (0.10) 0.10 (0.11)  
 Range (−0.20–0.13) (− 0.02–0.31)  
Non-Sitters
 n 5 51 9
 Mean Score (SD) 0.06 (0.10) 0.12 (0.12) 0.14 (0.13)
 Range (−0.03–0.21) (− 0.16–0.41) (− 0.10–0.34)
Sitters
 n 4 81 41
 Mean Score (SD) 0.11 (0.21) 0.26 (0.16) 0.23 (0.11)
 Range (−0.14–0.35) (−0.20–0.70) (0.04–0.48)
Walk with Support
 n 0 6 13
 Mean Score (SD)   0.44 (0.12) 0.35 (0.21)
 Range   (0.32–0.59) (0.02–0.63)
Walk Independently
 n 0 3 42
 Mean Score (SD)   0.58 (0.15) 0.64 (0.24)
 Range   (0.48–0.76) (−0.04–1)