Skip to main content

Table 2 HUI3 Scores by Functional Milestone and SMA Type

From: Quality of life data for individuals affected by spinal muscular atrophy: a baseline dataset from the Cure SMA Community Update Survey

Functional Status

Type I

Type II

Type III

Permanent Ventilation

 n

18

9

0

 Mean Score (SD)

− 0.05 (0.10)

0.10 (0.11)

 

 Range

(−0.20–0.13)

(− 0.02–0.31)

 

Non-Sitters

 n

5

51

9

 Mean Score (SD)

0.06 (0.10)

0.12 (0.12)

0.14 (0.13)

 Range

(−0.03–0.21)

(− 0.16–0.41)

(− 0.10–0.34)

Sitters

 n

4

81

41

 Mean Score (SD)

0.11 (0.21)

0.26 (0.16)

0.23 (0.11)

 Range

(−0.14–0.35)

(−0.20–0.70)

(0.04–0.48)

Walk with Support

 n

0

6

13

 Mean Score (SD)

 

0.44 (0.12)

0.35 (0.21)

 Range

 

(0.32–0.59)

(0.02–0.63)

Walk Independently

 n

0

3

42

 Mean Score (SD)

 

0.58 (0.15)

0.64 (0.24)

 Range

 

(0.48–0.76)

(−0.04–1)