Fig. 2From: Distal muscle weakness is a common and early feature in long-term enzyme-treated classic infantile Pompe patientsDistal muscle weakness of the feet and hands in ERT-treated classic infantile Pompe patients. a Severe weakness of foot dorsiflexor muscles, patient was asked to perform active dorsiflexion of the foot. b Weakness of finger extensor muscles, with characteristic positioning of the 3rd and 4th digit. Picture was taken at maximal finger extensionBack to article page