Table 1 General characteristics of patients
Patient ID | Gender | Age at study entry | Age at diagnosis | Years on ERT | Walton scale score | BMI before diet | Ventilatory support |
|---|---|---|---|---|---|---|---|
UD01 | M | 19 | 3 | 9 | 0 | 20.7 | no |
UD02 | M | 48 | 41 | 6 | 0 | 30.5 | no |
UD03 | F | 49 | 29 | 6 | 3 | 17.5 | no |
UD04 | M | 55 | 45 | 9 | 3 | NA | NIV |
UD05 | F | 46 | 25 | 9 | 6 | NA | NIV |
UD06 | F | 42 | 29 | 9 | 3 | 23.7 | NIV |
UD07 | F | 45 | 16 | 10 | 6 | 16.4 | NIV |
MI01 | F | 69 | 66 | 3 | 3 | 21 | no |
MI02 | M | 71 | 67 | 4 | 3 | 19.6 | NIV |
MI03 | F | 36 | 32 | 5 | 3 | 27.8 | no |
MI04 | F | 56 | 37 | 6 | 3 | NA | NIV |
MI05 | F | 59 | 54 | 5 | 3 | 28.4 | NIV |
MI06 | M | 51 | 45 | 6 | 2 | 22.3 | NIV |
Median ± IQR | 49.0 ± 11.0 | 37.0 ± 16.0 | 6.0 ± 4.0 | 21.65 ± 6.9 |