From: Lung function in Birt-Hogg-Dubé syndrome: a retrospective analysis of 96 patients
cases with available data, n | mean (SD) | abnormal values criterion | frequency of abnormal values, % | |
---|---|---|---|---|
FEV1, %pred | 96 | 97 (16) | < 80 | 8 |
FVC, %pred | 96 | 102 (16) | < 80 | 6 |
FEV1/FVC, % | 94 | 78 (7) | < 70 | 14 |
TLC, %pred | 70 | 103 (14) | < 80 / > 120 | 3 / 9 |
RV, %pred | 69 | 116 (36) | > 120 | 41 |
RV/TLC, % | 60 | 36 (9) | > 40 | 15 |
DLco, %pred | 69 | 85 (18) | < 80 | 33 |
DLco/VA, %pred | 70 | 94 (19) | < 80 | 24 |
PaO2, mmHg | 20 | 90 (9) | < 75 | 5 |