Maintenance of protein substitute intake is essential to help minimise catabolism during illness.|
It is better to give this in smaller, more frequent doses throughout the day.
Protein substitute given when there is a high temperature may lead to vomiting. It is always better to administer protein substitute when a high temperature is brought under control post administration of anti-pyretic medication.
|High carbohydrate intake||Encourage frequent high carbohydrate drinks or glucose polymer solution.|
|Natural protein intake||
If on dietary treatment only, there is no need to ‘formally’ omit natural protein. In practice, a reduced appetite leads to a lower natural protein intake.|
If on sapropterin (and dietary treatment), advice is the same as for dietary treatment only.
All treatment specific medication should be continued during illness.|
Medications should be free of aspartame.
Continue sapropterin if prescribed.
|Treat precipitating factors||Antibiotics (aspartame-free if possible)a.|
|Anti-pyretic medication||Give as necessary for high temperatures.|