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Table 1 Clinical and biochemical markers of metabolic control in GSDI patients and control subjects

From: Imbalanced cortisol concentrations in glycogen storage disease type I: evidence for a possible link between endocrine regulation and metabolic derangement

 

GSDIa

 

Controls

 

GSDIb

 

Controls

   

Mean

SE

Mean

SE

Mean

SE

Mean

SE

Ia vs C

Ib vs C

Age (years)

12.10

1.52

11.90

1.00

14.90

2.25

15.18

1.59

0.909

0.922

Fasting time (hours)

5.20

0.46

5.65

0.27

5.29

0.20

5.79

0.24

0.418

0.200

Height (cm)

139.00

5.80

144.70

4.00

143.00

4.00

155.00

3.40

0.420

0.040

Height (centile)

20.10

9.00

40.80

4.90

20.70

7.50

56.80

4.40

0.080

0.002

Weight (Kg)

46.80

6.60

49.70

4.40

54.90

7.40

61.70

5.20

0.710

0.460

Weight (centile)

68.00

7.70

72.00

4.10

75.70

6.60

87.80

1.20

0.610

0.030

BMI (Kg/m2)

22.93

1.30

23.05

10.80

25.90

2.12

25.00

1.44

0.947

0.734

BMI (centile)

88.80

3.20

88.80

2.20

92.00

2.40

91.90

2.03

0.811

0.520

Systolic BP (mmHg)

104.50

3.11

98.00

2.25

103.30

3.14

112.50

3.66

0.104

0.121

Diastolic BP (mmHg)

69.00

1.94

65.00

1.80

64.71

1.78

66.79

1.45

0.132

0.400

Glucose (mmol/L)

5.14

0.32

4.76

0.07

5.91

0.56

5.09

0.14

0.113

0.080

Cholesterol (mmol/L)

4.95

0.29

3.86

0.13

2.70

0.15

0.22

8.62

0.000

0.016

Triglycerides (TG) (mmol/L)

4.28

0.63

1.00

0.09

1.31

0.32

1.22

0.12

0.000

0.757

CChol (mmol/L)

4.09

0.20

3.66

0.12

2.44

0.11

3.33

0.21

0.090

0.010

Lactate (mmol/L)

2.16

0.15

1.33

0.05

3.26

0.67

1.35

0.06

0.000

0.000

Uric acid (μmol/L)

303.37

17.62

227.23

16.64

367.11

33.54

225.19

14.00

0.008

0.000

Bicarbonate (mmol/L)

22.40

0.71

26.31

0.43

20.77

1.14

24.57

0.48

0.000

0.002

  1. BP blood pressure, CChol corrected cholesterol