From: Increased visceral arterial tortuosity in Marfan syndrome
Groups | A (n = 5) | B (n = 12) | C (n = 20) | All (n = 37) |
---|---|---|---|---|
Age at CT (years) | 32.4 ± 2.6 | 37.5 ± 6.6 | 42.3 ± 14.3 | 39.4 ± 11.6 |
Male | 2 | 8 | 12 | 22 |
Involvement of cardiovascular system | No intervention required | Mild involvement required intervention | Severe cardiovascular involvement | Involvement of varying degree |
Anthropometric (measured) | ||||
Height (cm) | 184.0 [180.0-185.0] | 194.0 [182.0-199.2] | 187.5 [181.2-195.8] | 186.0 [181.5-197.5] |
Arm span (cm) | 183.0 [182.0-187.0] | 191.0 [189.0-210.0] | 186.0 [184.2-204.5] | 189.0 [183.0-204.0] |
Lower segment (cm) | 90.0 [90.0-99.0] | 95.0 [94.0-104.0] | 98.0 [93.2-99.8] | 97.0 [91.8-103.0] |
Foot size (cm) | 28.0 [25.3-28.0] | 29.0 [26.7-30.2] | 27.7 [26.7-29.7] | 28.0 [26.7-30.0] |
Weight (kg) | 70.0 [60.0-72.0] | 74.0 [63.8-93.5] | 82.0 [72.8-96.5] | 75.0 [65.0-93.0] |
Anthropometric (calculated) | ||||
Arm span to height ratio | 1.01 [1.01-1.02] | 1.02 [1.00-1.04] | 1.02 [1.01-1.07] | 1.02 [1.01-1.05] |
Upper segment to lower segment ratio | 1.00 [0.82-1.06] | 0.92 [0.84-0.96] | 0.90 [0.86-0.97] | 0.92 [0.85-1.01] |
Body Mass Index (BMI; kg/m2) | 20.5 [18.5-21.3] | 20.6 [19.6-24.1] | 23.0 [21.4-26.0] | 21.5 [19.6-25.2] |
Body surface area (m2) - Mosteller | 1.90 [1.73-1.92] | 2.01 [1.81-2.27] | 2.08 [1.92-2.26] | 1.97 [1.81-2.26] |
Ghent nosology | ||||
Positive family history (%) | 80.0% | 58.3% | 35.0% | 48.6% |
Systemic score (SSc)* | 5.0 [2.0-7.0] | 8.0 [6.5-9.0] | 8.0 [5.8-9.0] | 8.0 [5.0-9.0] |
SSc < 7 pts. (%) | 60.0% | 25.0% | 30.0% | 32.4% |
SSc 7-10 pts. (%) | 40.0% | 58.3% | 65.0% | 59.5% |
SSc > 10 pts. (%) | 0.0% | 16.7% | 5.0% | 8.1% |
Risk factors for atherosclerosis | ||||
Hypertension (%) | 0.0 | 66.7 | 25.0 | 35.1 |
Hyperlipidemia (%) | 0.0 | 8.3 | 15.0 | 10.8 |
Smoking (%) | 0.0 | 25.0 | 5.0 | 10.8 |
Diabetes (%) | 0.0 | 0.0 | 5.0 | 2.7 |
History of coronary artery disease (%) | 0.0 | 0.0 | 5.0 | 2.7 |