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Table 1 Patient characteristics of the severity groups of Marfan syndrome patients including the presence of risk factors for atherosclerosis

From: Increased visceral arterial tortuosity in Marfan syndrome

Groups

A (n = 5)

B (n = 12)

C (n = 20)

All (n = 37)

Age at CT (years)

32.4 ± 2.6

37.5 ± 6.6

42.3 ± 14.3

39.4 ± 11.6

Male

2

8

12

22

Involvement of cardiovascular system

No intervention required

Mild involvement required intervention

Severe cardiovascular involvement

Involvement of varying degree

Anthropometric (measured)

 Height (cm)

184.0 [180.0-185.0]

194.0 [182.0-199.2]

187.5 [181.2-195.8]

186.0 [181.5-197.5]

 Arm span (cm)

183.0 [182.0-187.0]

191.0 [189.0-210.0]

186.0 [184.2-204.5]

189.0 [183.0-204.0]

 Lower segment (cm)

90.0 [90.0-99.0]

95.0 [94.0-104.0]

98.0 [93.2-99.8]

97.0 [91.8-103.0]

 Foot size (cm)

28.0 [25.3-28.0]

29.0 [26.7-30.2]

27.7 [26.7-29.7]

28.0 [26.7-30.0]

 Weight (kg)

70.0 [60.0-72.0]

74.0 [63.8-93.5]

82.0 [72.8-96.5]

75.0 [65.0-93.0]

Anthropometric (calculated)

 Arm span to height ratio

1.01 [1.01-1.02]

1.02 [1.00-1.04]

1.02 [1.01-1.07]

1.02 [1.01-1.05]

 Upper segment to lower segment ratio

1.00 [0.82-1.06]

0.92 [0.84-0.96]

0.90 [0.86-0.97]

0.92 [0.85-1.01]

 Body Mass Index (BMI; kg/m2)

20.5 [18.5-21.3]

20.6 [19.6-24.1]

23.0 [21.4-26.0]

21.5 [19.6-25.2]

 Body surface area (m2) - Mosteller

1.90 [1.73-1.92]

2.01 [1.81-2.27]

2.08 [1.92-2.26]

1.97 [1.81-2.26]

Ghent nosology

 Positive family history (%)

80.0%

58.3%

35.0%

48.6%

 Systemic score (SSc)*

5.0 [2.0-7.0]

8.0 [6.5-9.0]

8.0 [5.8-9.0]

8.0 [5.0-9.0]

 SSc < 7 pts. (%)

60.0%

25.0%

30.0%

32.4%

 SSc 7-10 pts. (%)

40.0%

58.3%

65.0%

59.5%

 SSc > 10 pts. (%)

0.0%

16.7%

5.0%

8.1%

Risk factors for atherosclerosis

 Hypertension (%)

0.0

66.7

25.0

35.1

 Hyperlipidemia (%)

0.0

8.3

15.0

10.8

 Smoking (%)

0.0

25.0

5.0

10.8

 Diabetes (%)

0.0

0.0

5.0

2.7

 History of coronary artery disease (%)

0.0

0.0

5.0

2.7

  1. *SSc Systemic score