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Table 1 Patient characteristics of the severity groups of Marfan syndrome patients including the presence of risk factors for atherosclerosis

From: Increased visceral arterial tortuosity in Marfan syndrome

GroupsA (n = 5)B (n = 12)C (n = 20)All (n = 37)
Age at CT (years)32.4 ± 2.637.5 ± 6.642.3 ± 14.339.4 ± 11.6
Male281222
Involvement of cardiovascular systemNo intervention requiredMild involvement required interventionSevere cardiovascular involvementInvolvement of varying degree
Anthropometric (measured)
 Height (cm)184.0 [180.0-185.0]194.0 [182.0-199.2]187.5 [181.2-195.8]186.0 [181.5-197.5]
 Arm span (cm)183.0 [182.0-187.0]191.0 [189.0-210.0]186.0 [184.2-204.5]189.0 [183.0-204.0]
 Lower segment (cm)90.0 [90.0-99.0]95.0 [94.0-104.0]98.0 [93.2-99.8]97.0 [91.8-103.0]
 Foot size (cm)28.0 [25.3-28.0]29.0 [26.7-30.2]27.7 [26.7-29.7]28.0 [26.7-30.0]
 Weight (kg)70.0 [60.0-72.0]74.0 [63.8-93.5]82.0 [72.8-96.5]75.0 [65.0-93.0]
Anthropometric (calculated)
 Arm span to height ratio1.01 [1.01-1.02]1.02 [1.00-1.04]1.02 [1.01-1.07]1.02 [1.01-1.05]
 Upper segment to lower segment ratio1.00 [0.82-1.06]0.92 [0.84-0.96]0.90 [0.86-0.97]0.92 [0.85-1.01]
 Body Mass Index (BMI; kg/m2)20.5 [18.5-21.3]20.6 [19.6-24.1]23.0 [21.4-26.0]21.5 [19.6-25.2]
 Body surface area (m2) - Mosteller1.90 [1.73-1.92]2.01 [1.81-2.27]2.08 [1.92-2.26]1.97 [1.81-2.26]
Ghent nosology
 Positive family history (%)80.0%58.3%35.0%48.6%
 Systemic score (SSc)*5.0 [2.0-7.0]8.0 [6.5-9.0]8.0 [5.8-9.0]8.0 [5.0-9.0]
 SSc < 7 pts. (%)60.0%25.0%30.0%32.4%
 SSc 7-10 pts. (%)40.0%58.3%65.0%59.5%
 SSc > 10 pts. (%)0.0%16.7%5.0%8.1%
Risk factors for atherosclerosis
 Hypertension (%)0.066.725.035.1
 Hyperlipidemia (%)0.08.315.010.8
 Smoking (%)0.025.05.010.8
 Diabetes (%)0.00.05.02.7
 History of coronary artery disease (%)0.00.05.02.7
  1. *SSc Systemic score