Fig. 3
From: 2-methylacetoacetyl-coenzyme A thiolase (beta-ketothiolase) deficiency: one disease - two pathways
Number of acute decompensations in 221 MATD patients. Around 90% of patients experienced at least one acute metabolic crisis. Patients without acute decompensations were mostly identified by newborn screening or family screening. *This category comprises patients with exactly one decompensation and those with at least one decompensation if no further details were given