Table 2 Frequencies of autoantibodies against complement proteins in patients affected by BSS
From: Immunological features of patients affected by Barraquer-Simons syndrome
C3NeF | anti-C3 | anti-FB | anti-P | anti-FI | anti-FH | C3 (mg/dl) | |
|---|---|---|---|---|---|---|---|
BSS1 | Positive | Positive | Negative | Negative | Negative | Negative | 3.0 |
BSS2 | Positive | Positive | Negative | Negative | Negative | Negative | 11.9 |
BSS3 | Positive | Positive | Positive | Positive | Negative | Negative | 31.7 |
BSS4 | Positive | Positive | Negative | Negative | Negative | Negative | 7.9 |
BSS5 | Positive | Negative | Negative | Negative | Negative | Negative | 14.8 |
BSS6 | Negative | Negative | Negative | Negative | Negative | Negative | 88.5 |
BSS7 | Positive | Negative | Positive | Positive | Negative | Negative | 38.7 |
BSS8 | Negative | Negative | Negative | Negative | Negative | Negative | 121.0 |
BSS9 | Positive | Negative | Positive | Positive | Negative | Negative | 20.6 |
BSS10 | Positive | Negative | Positive | Positive | Negative | Negative | 50.2 |
BSS11 | Negative | Negative | Negative | Negative | Negative | Negative | 127.0 |
BSS12 | Positive | Negative | Negative | Positive | Negative | Negative | 8.9 |
BSS13 | Negative | Negative | Negative | Negative | Negative | Negative | 113.0 |
9/13 (69.2%) | 4/13 (30.8%) | 4/13 (30.8%) | 5/13 (38.5%) | 0/13 (0%) | 0/13 (0%) | Range: 75–135 mg/dl |