From: Evaluation of retinal microvascular perfusion in hereditary angioedema: a case-control study
HAE (n = 20) | HC (n = 20) | |
---|---|---|
Age (years) | 41.3 ± 13.5 | 45 ± 13 |
Female sex (N/%) | 10/50 | 11/55 |
HAE disease duration (years) | 27.4 ± 14 | N.A. |
Number of attacksa | 8 ± 7.6 | N.A. |
Attack-free period (days)b | 59 ± 71 | N.A. |
Danazol prohylaxis (N/%) | 4/20 | N.A. |
C4 (mg/dl) | 9.5 ± 4.5 | N.A. |
C1q (mg/l) | 146 ± 20.3 | N.A. |
C1INH (mg/dl) | 7 ± 3.4 | N.A. |
C1INH (%) | 27.6 ± 12.2 | N.A. |
MABP (mmHg) | 89 ± 10.4 | 88 ± 8 |
BCVA (LogMAR) | 0.01 ± 0.1 (R); 0.01 ± 0.1 (L) | 0.013 ± 0.03 |
IOP (mmHg) | 16.5 ± 3 (R); 16.7 ± 2.9 (L) | 16 ± 3 |
MD (median, dB) | −1.9 ***(R); − 2 ***(L) | 0.3 |
PSD (median, dB) | 2.16 **(R); 1.9 *(L) | 1.6 |
VFI (range %) | 92–98 | 98–100 |