C4NeF positive patients n = 17 | C4NeF negative patients n = 102 | p | |
---|---|---|---|
serum C4 (0.15–0.55 g/L) | 0.2 (0.12–0.26) | 0.23 (0.17–0.32) | 0.232 |
serum C3 (0.9–1.8 g/L) | 0.33 (0.19–0.98) | 0.73 (0.39–01) | 0.115 |
Classical pathway activity (48–103 CH50/mL) | 30 (11–54) | 46 (28–61) | 0.065 |
Alternative pathway activity (70–125%) | 40 (0–67) | 63 (3–87) | 0.055 |
C3NeF positivity (< 10%) | 7(41) | 20 (19.6) | 0.063 |
C1q (60–180 mg/L) | 108 (83–138) | 102 (83–123) | 0.528 |
anti-C1q (< 52 U/mL) | 4 (23.5) | 10 (9.8) | 0.117 |
C4d (0.7–6.3 ng/mL) | 3.23 (2.6–5.3) | 5.46 (3.15–9.27) | 0.038 |