Table 1 Demographic and Clinical Characteristics of patients with KLA and KHE a
From: Kaposiform lymphangiomatosis and kaposiform hemangioendothelioma: similarities and differences
Variables | KLA | KHE |
|---|---|---|
n = 6 | n = 7 | |
Patients | ||
Genderb | ||
Male | 2 (33.3) | 2 (28.6) |
Female | 4 (66.7) | 5 (71.4) |
Age at the time of the presentation of the signs and/or symptoms (m) | ||
Mean (range) | 26.7 (8.0–72.0) | 4.1 (0.0–10.0) |
Age at diagnosis (m) | ||
Mean (range) | 52.8 (13.0–108.0) | 6.5 (0.3–14.0) |
Vascular lesions | ||
Involvementb | ||
Skin | 1 (16.7) | 4 (57.1) |
Lung | 5 (83.3) | 0 (0.0) |
Bones | 4 (66.7) | 4 (57.1) |
Peritoneal cavity | 3 (6.3) | 0 (0.0) |
Manifestationb | ||
Focal | 0 (0.0) | 6 (85.7) |
Multifocal | 0 (0.0) | 1 (14.3) |
Diffuse | 6 (100.0) | 0 (0.0) |
Follow-up (y) | ||
Mean (range) | 4.8 (3.2–6.0) | 4.3 (1.2–9.0) |
Outcomeb | ||
Improved | 1 (16.7) | 6 (85.7) |
Stable | 1 (16.7) | 0 (0.0) |
Worse | 2 (33.3) | 0 (0.0) |
Death | 2 (33.3) | 1 (14.3) |