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Table 1 Demographic and clinical characteristics of 202 subjects with Wilson disease included in the study population

From: Social and demographic characteristics of a Polish cohort with Wilson disease and the impact of treatment persistence

Variable n = 202 Values
Male:female ratio, n (%) 93 (46):109 (54)
Age, mean ± SD (years) 36.4 ± 9.9
Age at diagnosis, mean ± SD (years) 25.8 ± 9.8
Latency period,a mean ± SD (months) 14.2 ± 12.0
Length of treatment, mean ± SD (years) 11.0 ± 3.2
Predominant clinical form, n (%)
 - Pre-symptomatic 22 (10.9)
 - Hepatic 73 (36.1)
 - Neurological 107 (53.0)
Drug compliance (persistence),b n (%)
 Yes 139c (72.4)
 No 53 (27.6)
  1. SD standard deviation
  2. aThe period since first clinical symptoms
  3. bPatients were considered non-persistent if they had at least one break of ≥3 months or more than 2 breaks lasting for ≥2 months within the last 3 years of treatment
  4. c10 patients received liver transplants and stopped taking medication for Wilson disease