Table 1 Initial clinical characteristics of all SS patients included in this review, the 47 patients whose treatment was described and the 30 patients treated with corticosteroids
All patients N = 64 | Patients where treatment was specified N = 47 | Patients treated with corticosteroids N = 30 | |
|---|---|---|---|
Age of onset | 13.02 ± 9.08 | 14.19 ± 10.35 | 13.80 ± 10.32 |
Female sex | 47/64 (73%) | 35/47 (74%) | 23/30 (77%) |
Muscle manifestations | 100% | 100% | 100% |
Alopecia | 100% | 100% | 100% |
Alopecia universalis | 40/64 (63%) | 25/47 (53%) | 17/30 (57%) |
Diarrhea | 37/64 (58%) | 26/47 (55%) | 17/30 (57%) |
Weight loss, low weight or growth retardation | 33/64 (52%) | 23/47 (49%) | 14/30 (47%) |
Skeletal alterations | 22/64 (34%) | 16/47 (34%) | 10/30 (33%) |
Amenorrhea | 23/47 (49%) | 15/35 (43%) | 9/23 (39%) |
ANA + | 17/64 (27%) | 17/47 (36%) | 13/30 (43%) |
Other autoantibodies | 15/64 (23%) | 15/47 (32%) | 11/30 (37%) |
Deaths | 7 (11%) | 2 (4%) | 0 (0%) |