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Table 5 The values of echocardiographic parameters of the 26 patients with MPS III

From: Cardiac characteristics and natural progression in Taiwanese patients with mucopolysaccharidosis III

Echocardiographic parameters

LVMI (z score)

RVDd (z score)

IVSd (z score)

IVSs (z score)

LVIDd (z score)

LVIDs (z score)

LVPWd (z score)

LVPWs (z score)

AoD (z score)

LAD (z score)

Mean

−0.36

0.80

1.71

0.39

−0.06

−0.44

0.15

−0.19

1.62

−0.44

SD

0.94

1.41

1.62

0.61

1.15

1.09

1.12

1.03

1.57

1.31

Z score > 2 (%)

0%

16%

38%

0%

0%

0%

8%

5%

27%

4%

  1. MPS Mucopolysaccharidosis, LVMI Left ventricular mass index, RVDd Right ventricular end-diastolic dimension, IVSd Interventricular septal end-diastolic dimension, IVSs Interventricular septal end-systolic dimension, LVIDd Left ventricular end-diastolic dimension, LVIDs Left ventricular end-systolic dimension, LVPWd Left ventricular posterior wall end-diastolic dimension, LVPWs Left ventricular posterior wall end-systolic dimension, AoD Aortic diameter, LAD Left atrial dimension, SD Standard deviation