From: Cardiac characteristics and natural progression in Taiwanese patients with mucopolysaccharidosis III
Echocardiographic features | MS | MR | AS | AR | MVP | Thick IVS |
---|---|---|---|---|---|---|
n (%) | 2 (8%) | 8 (31%) | 2 (8%) | 5 (19%) | 3 (12%) | 5 (19%) |
r value (severity of cardiac valve abnormalities versus age) | 0.211 | 0.272 | 0.357 | 0.375 | −0.171 | −0.218 |
p value | p > 0.05 | p > 0.05 | p > 0.05 | p < 0.05 | p > 0.05 | p > 0.05 |