| Mean ± SD | ||
---|---|---|---|
This study | Harmatz et al. [15] | Lin et al. [16] | |
6-MWT | |||
 0–4 years old | 246.9 m (n = 1) | 251.6 ± 121.5 m (n = 37) | – |
 5–11 years old | 218.8 ± 98.2 m (n = 4) | 232.5 ± 140.1 m (n = 127) | – |
 12–18 years old | 123.7 ± 116.4 m (n = 5) | 181.2 ± 177.3 m (n = 84) | – |
 > 18 years old | 119.3 ± 121.2 m (n = 3) | 193.1 ± 148.5 m (n = 68) | – |
 Overall 6-MWTa | 161.4 ± 110.1 m (n = 13) | 212.6 ± 152.2 m (n = 316) | 235.3 ± 125.5 m (n = 11) |
 Overall age | 15.5 ± 8.1 years | 14.5 years | 12.6 ± 6.6 years |
Spirometry, FVC | |||
 ≤ 18 years old | 0.6 ± 0.1 L (n = 5) | 1.1 ± 0.7 L (n = 256) | – |
 > 18 years old | 0.9 ± 0.2 L (n = 3) | 1.5 ± 1.1 L (n = 69) | – |